Citation Impact
Citing Papers
SuFEx-enabled, agnostic discovery of covalent inhibitors of human neutrophil elastase
2019 StandoutNobel
A double-blind randomized placebo-controlled phase III study of a Pseudomonas aeruginosa flagella vaccine in cystic fibrosis patients
2007
The Pseudomonas aeruginosa accessory genome elements influence virulence towards Caenorhabditis elegans
2019 StandoutNobel
Aerosolized colistin for the treatment of nosocomial pneumonia due to multidrug-resistant Gram-negative bacteria in patients without cystic fibrosis
2004
The clinical impact of bacterial biofilms
2011
Cystic Fibrosis Foundation Pulmonary Guideline. Pharmacologic Approaches to Prevention and Eradication of Initial Pseudomonas aeruginosa Infection
2014
Antibiotic Management of Lung Infections in Cystic Fibrosis. I. The Microbiome, Methicillin-Resistant Staphylococcus aureus , Gram-Negative Bacteria, and Multiple Infections
2014
Engineering precision nanoparticles for drug delivery
2020 Standout
SharedPseudomonas aeruginosagenotypes are common in Australian cystic fibrosis centres
2012
Role of magnesium in the failure of rhDNase therapy in patients with cystic fibrosis
2006
Variant Cystic Fibrosis Phenotypes in the Absence ofCFTRMutations
2002
The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) statement: guidelines for reporting observational studies
2008 Standout
Determination of the Minimal Clinically Important Difference Scores for the Cystic Fibrosis Questionnaire-Revised Respiratory Symptom Scale in Two Populations of Patients With Cystic Fibrosis and Chronic Pseudomonas aeruginosa Airway Infection
2009
Loss of Cystic Fibrosis Transmembrane Conductance Regulator Function Produces Abnormalities in Tracheal Development in Neonatal Pigs and Young Children
2010
Cystic Fibrosis Pulmonary Guidelines
2009
The Retinal Pigment Epithelium in Visual Function
2005 Standout
Eradication of early Pseudomonas aeruginosa infection
2005
Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508delCFTR
2015 Standout
Exercise with incorporated expiratory manoeuvres was as effective as breathing techniques for airway clearance in children with cystic fibrosis: a randomised crossover trial
2012
THERAPIES AIMED AT AIRWAY INFLAMMATION IN CYSTIC FIBROSIS
1998
Understanding how cystic fibrosis mutations disrupt CFTR function: From single molecules to animal models
2014
Hidradenitis Suppurativa
2012 Standout
Cystic fibrosis
2016 Standout
Gene therapy for cystic fibrosis: challenges and future directions.
1995
Cystic fibrosis
2003
Pancreatic enzyme replacement therapy for people with cystic fibrosis
2014
Better reporting of interventions: template for intervention description and replication (TIDieR) checklist and guide
2014 Standout
Managing Cystic Fibrosis
2011
Pulmonary fibrosis: pathogenesis, etiology and regulation
2009 Standout
The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) Statement: Guidelines for reporting observational studies
2014 Standout
Genotype and Phenotype in Cystic Fibrosis
2000
Clinical Epidemiological Quality in Molecular Genetic Research
1999
Cystic Fibrosis Pulmonary Guidelines
2007
Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study
2003
Colistin: the re-emerging antibiotic for multidrug-resistant Gram-negative bacterial infections
2006
Multidetector Computed Tomography for Acute Pulmonary Embolism
2006 Standout
New insights into cystic fibrosis-related diabetes in children
2013
Effects of Gender and Age at Diagnosis on Disease Progression in Long-term Survivors of Cystic Fibrosis
2010
Allergic Bronchopulmonary Aspergillosis in Cystic Fibrosis—State of the Art: Cystic Fibrosis Foundation Consensus Conference
2003
Effects of extracellular matrix viscoelasticity on cellular behaviour
2020 StandoutNature
Predicting the Functional Effect of Amino Acid Substitutions and Indels
2012 Standout
Emerging bacterial pathogens and changing concepts of bacterial pathogenesis in cystic fibrosis
2015
Pseudomonas aeruginosa Exhibits Frequent Recombination, but Only a Limited Association between Genotype and Ecological Setting
2012
European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis
2014
British Thoracic Society guidelines for the management of non-tuberculous mycobacterial pulmonary disease (NTM-PD)
2017 Standout
Modifier genes in Mendelian disorders: the example of cystic fibrosis
2010
Nonresolving Inflammation
2010 Standout
Antibiotic resistance of bacterial biofilms
2010 Standout
Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience
2008
Human airway surface epithelial regeneration is delayed and abnormal in cystic fibrosis
2006
Cystic Fibrosis
2005
Innate Immunity and Asthma Risk in Amish and Hutterite Farm Children
2016 Standout
A CFTR Potentiator in Patients with Cystic Fibrosis and the G551D Mutation
2011 Standout
A contemporary survival analysis of individuals with cystic fibrosis: a cohort study
2014
Bacterial biofilms: from the Natural environment to infectious diseases
2004 Standout
Airways Reactivity in Patients with CF
2002
Pharmacological approaches for the discovery and development of new anti-inflammatory agents for the treatment of cystic fibrosis
2002
PEGylation as a strategy for improving nanoparticle-based drug and gene delivery
2015 Standout
Early intervention and prevention of lung disease in cystic fibrosis: a European consensus
2004
Evaluating the “Leeds criteria” forPseudomonas aeruginosainfection in a cystic fibrosis centre
2006
Reduced risk of nontuberculous mycobacteria in cystic fibrosis adults receiving long-term azithromycin
2015
A randomized controlled trial of high-dose ursodesoxycholic acid for nonalcoholic steatohepatitis
2010
The prevalence of cystic fibrosis in the European Union
2008
Genotype–phenotype correlation in cystic fibrosis: The role of modifier genes
2002
Intestinal mucosal barrier function in health and disease
2009 Standout
US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis
2015
Post-antibiotic and post- -lactamase inhibitor effects of ceftazidime plus sulbactam on extended-spectrum -lactamase-producing Gram-negative bacteria
2004
Cystic fibrosis
1998
Synthetic hydrogels for human intestinal organoid generation and colonic wound repair
2017
Beclomethasone diproprionate reduced airway inflammation without adrenal suppression in young children with cystic fibrosis: A pilot study†‡
2001
European Cystic Fibrosis Society Standards of Care: Best Practice guidelines
2014
US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis: executive summary
2015
Antimicrobial resistance in the respiratory microbiota of people with cystic fibrosis
2014
Pulmonary Complications of Cystic Fibrosis
2009
Cystic fibrosis genetics: from molecular understanding to clinical application
2014 Standout
Randomised controlled trial of inhaled corticosteroids (fluticasone propionate) in cystic fibrosis
1997
Cystic Fibrosis Pulmonary Guidelines
2013
Aminoglycoside use in cystic fibrosis: therapeutic strategies and toxicity
2010
CFTR Genotype as a Predictor of Prognosis in Cystic Fibrosis
2006
Alternative Activation of Macrophages: Mechanism and Functions
2010 Standout
Nontuberculous mycobacteria
2013
Airway Mucus Function and Dysfunction
2010 Standout
The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) Statement: Guidelines for Reporting Observational Studies
2007 Standout
Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders
2008
The diagnosis and management of non-alcoholic fatty liver disease: Practice Guideline by the American Association for the Study of Liver Diseases, American College of Gastroenterology, and the American Gastroenterological Association
2012 Standout
Analysis of structural and biochemical events occurring in the small intestine after dietary polyamine ingestion in suckling rats
1996
End of life care for patients with cystic fibrosis
2011
Hospital-Acquired Infections Due to Gram-Negative Bacteria
2010 Standout
CFTR2: How will it help care?
2013
Allele specific repair of splicing mutations in cystic fibrosis through AsCas12a genome editing
2019
Inhaled Aztreonam Lysine for Chronic Airway Pseudomonas aeruginosa in Cystic Fibrosis
2008
Update on Key Emerging Challenges in Cystic Fibrosis
2014 Standout
Immunomodulatory Effects of Macrolide Antibiotics – Part 1: Biological Mechanisms
2010
Antimicrobial peptides: therapeutic potential
2006
Efficacy and safety of aerosolized tobramycin in cystic fibrosis
2001
The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) statement: guidelines for reporting observational studies
2007 Standout
The Role of Inflammation in the Pathophysiology of CF Lung Disease
2002
Technical Report: Precautions Regarding the Use of Aerosolized Antibiotics
2000
Ion Channels — Basic Science and Clinical Disease
1997
Treatment of early Pseudomonas aeruginosa infection in patients with cystic fibrosis: the ELITE trial
2009
ClinVar: public archive of interpretations of clinically relevant variants
2015 Standout
Cystic fibrosis
2009
The genetics of asthma and allergic disease: a 21st century perspective
2011
Erm(41)-dependent inducible resistance to azithromycin and clarithromycin in clinical isolates of Mycobacterium abscessus
2014
Pseudomonas aeruginosa Population Structure Revisited
2009
Clinical Features Associated with a Delayed Diagnosis of Cystic Fibrosis
2000
Modeling Development and Disease with Organoids
2016 Standout
Pulmonary Function and Clinical Observations in Men With Congenital Bilateral Absence of the Vas Deferens
1996
Antibiotic and Anti-Inflammatory Therapies for Cystic Fibrosis
2013
Antimicrobial and host-defense peptides as new anti-infective therapeutic strategies
2006 Standout
The Use of Anti-inflammatory Medications in Cystic Fibrosis
1999
Identifying Treatments That Halt Progression of Pulmonary Disease in Cystic Fibrosis
1997
Macrolide antibiotic therapy in patients with cystic fibrosis
2003
Evidence that Systemic Gentamicin Suppresses Premature Stop Mutations in Patients with Cystic Fibrosis
2001
Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis
2003 Standout
Staphylococcus aureus Infections: Epidemiology, Pathophysiology, Clinical Manifestations, and Management
2015 Standout
Acinetobacter baumannii : Emergence of a Successful Pathogen
2008 Standout
Changes in Cystic Fibrosis Airway Microbial Community Associated with a Severe Decline in Lung Function
2015
Practical Guidelines: Lung Transplantation in Patients with Cystic Fibrosis
2014
Magnesium in Man: Implications for Health and Disease
2014 Standout
Azithromycin Blocks Quorum Sensing and Alginate Polymer Formation and Increases the Sensitivity to Serum and Stationary-Growth-Phase Killing ofPseudomonas aeruginosaand Attenuates ChronicP. aeruginosaLung Infection inCftr−/−Mice
2007
Inhaled steroids for bronchiectasis
2009
Sensitivity and Specificity of Helical Computed Tomography in the Diagnosis of Pulmonary Embolism
2000
Transport of Nanoparticles in Cystic Fibrosis Sputum and Bacterial Biofilms by Single-Particle Tracking Microscopy
2012
Prevalence and Clinical Significance of Staphylococcus aureus Small-Colony Variants in Cystic Fibrosis Lung Disease
2006
Implications of Rewiring Bacterial Quorum Sensing
2007 StandoutNobel
Bacterial Biofilms: A Common Cause of Persistent Infections
1999 StandoutScience
Bacterial Resistance to β-Lactam Antibiotics: Compelling Opportunism, Compelling Opportunity
2005 Standout
The diagnosis and management of nonalcoholic fatty liver disease: Practice guidance from the American Association for the Study of Liver Diseases
2017 Standout
Chloride secretion in the trachea of null cystic fibrosis mice: the effects of transfection with pTrial10‐CFTR2.
1997 StandoutNobel
Infection control recommendations for patients with cystic fibrosis: Microbiology, important pathogens, and infection control practices to prevent patient-to-patient transmission
2003
Spermidine in health and disease
2018 StandoutScience
Role of CFTR in Airway Disease
1999
Potential of preventing Pseudomonas aeruginosa lung infections in cystic fibrosis patients: Experimental studies in animals
1996
Wound Healing: A Cellular Perspective
2018 Standout
Antibiotic Management of Methicillin-Resistant Staphylococcus aureus–Associated Acute Pulmonary Exacerbations in Cystic Fibrosis
2015
Antibiotic Susceptibilities of Pseudomonas aeruginosa Isolates Derived from Patients with Cystic Fibrosis under Aerobic, Anaerobic, and Biofilm Conditions
2005
Cystic fibrosis: An update for clinicians. Part 1: Nutrition and gastrointestinal complications
2014
The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) Statement: Guidelines for Reporting Observational Studies
2007 Standout
Clinical Practice Guideline (Update): Adult Sinusitis
2015 Standout
Azithromycin Inhibits the Formation of Flagellar Filaments without Suppressing Flagellin Synthesis in Salmonella enterica Serovar Typhimurium
2005 StandoutNobel
Diagnosis of Nontuberculous Mycobacterial Infections
2013
Lung Infections Associated with Cystic Fibrosis
2002 Standout
Photothermal Nanomaterials: A Powerful Light-to-Heat Converter
2023 Standout
Changing epidemiology and clinical issues arising in an ageing cystic fibrosis population
2010
Works of Harry Heijerman being referenced
European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre
2014
Transmission of Pseudomonas aeruginosa in children with cystic fibrosis attending summer camps in The Netherlands
2007
Antibiotic therapy against Pseudomonas aeruginosa in cystic fibrosis: a European consensus
2000
Demographics of glucose metabolism in cystic fibrosis
2009
Oxygen-assisted exercise training in adult cystic fibrosis patients with pulmonary limitation to exercise
1991
Comparison of a high lipase pancreatic enzyme extract with a regular pancreatin preparation in adult cystic fibrosis patients
1994
Nutrition in patients with cystic fibrosis: a European Consensus
2002
Multicenter, open-label study of recombinant human DNase in cystic fibrosis patients with moderate lung disease
1998
Improvement of fecal fat excretion after addition of omeprazole to pancrease in cystic fibrosis is related to residual exocrine function of the pancreas
1993
Clinical trials in cystic fibrosis
2007
No hearing loss after repeated courses of tobramycin in cystic fibrosis patients
2010
Pharmacokinetics and sputum penetration of azithromycin during once weekly dosing in cystic fibrosis patients
2007
Azithromycin maintenance therapy in patients with cystic fibrosis: A dose advice based on a review of pharmacokinetics, efficacy, and side effects
2012
Birth Prevalence and Survival in Cystic Fibrosis
2005
Infection and inflammation in cystic fibrosis: A short review
2005
Low-Dose versus High-Dose Ursodeoxycholic Acid in Cystic Fibrosis-Related Cholestatic Liver Disease Results of a Randomized Study with 1-Year Follow-up
1997
Dry powder inhalation of antibiotics in cystic fibrosis therapy: part 2
2002
The effects of the inhaled corticosteroid budesonide on lung function and bronchial hyperresponsiveness in adult patients with cystic fibrosis
1995
Importance of bacteriology in upper airways of patients with Cystic Fibrosis
2013
Outcome of assisted ventilation for acute respiratory failure in cystic fibrosis
2006
Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: A European consensus
2009
Microvascular complications in patients with cystic fibrosis-related diabetes (CFRD)
2008
Effect of nebulized colistin sulphate and colistin sulphomethate on lung function in patients with cystic fibrosis: a pilot study
2004
Pharmacokinetics of Azithromycin in Plasma, Blood, Polymorphonuclear Neutrophils and Sputum During Long-Term Therapy in Patients With Cystic Fibrosis
2006
Pharmacokinetics of Ceftazidime in Adult Cystic Fibrosis Patients During Continuous Infusion and Ambulatory Treatment at Home
1994
Risk factors for Mycobacterium abscessus infection in cystic fibrosis patients; a case–control study
2012
Can helical CT replace scintigraphy in the diagnostic process in suspected pulmonary embolism? A retrolective-prolective cohort study focusing on total diagnostic yield
1998
A Cystic Fibrosis Mutation Associated with Mild Lung Disease
1995
Vestibulotoxicity as a consequence of systemically administered tobramycin in cystic fibrosis patients
2008
Standards of care for patients with cystic fibrosis: a European consensus
2005
Effect of rhDNase on lung function and quality of life in adult cystic fibrosis patients
1995
Treatment of lung infection in patients with cystic fibrosis: Current and future strategies
2012
Pseudomonas aeruginosa Genotype Prevalence in Dutch Cystic Fibrosis Patients and Age Dependency of Colonization by Various P. aeruginosa Sequence Types
2009
Antibiotic treatment in cystic fibrosis
2000
Genetic and clinical features of patients with cystic fibrosis diagnosed after the age of 16 years.
1995
Characterizing responses to CFTR-modulating drugs using rectal organoids derived from subjects with cystic fibrosis
2016
Pharmacokinetics of aerosolized tobramycin in adult patients with cystic fibrosis
1997
Pseudomonas aeruginosa Genotype Prevalence in Dutch Cystic Fibrosis Patients and Age Dependency of Colonization by Various P. aeruginosa Sequence Types
2012